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High flow nasal oxygenation and videolaryngoscopy - the two saviours in a case of Prader-Willi syndrome: A case report

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Case Report

Author Details : Aparna Singh, Prachi Gaba*, Kush Sharma, Lalit Gupta

Volume : 11, Issue : 4, Year : 2024

Article Page : 608-610

https://doi.org/10.18231/j.ijca.2024.109

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Abstract

Prader-Willi syndrome (PWS) is a rare genetic disorder characterized by hypothalamic-pituitary abnormalities, hypotonia, hyperphagia, and a high risk of morbid obesity, which complicates both general and regional anesthesia. Patients with PWS face additional challenges, including disturbances in thermoregulation, arrhythmias, cor pulmonale, and convulsions. These factors make anesthetic management particularly challenging, necessitating careful planning and monitoring.We report the anesthetic management of a 7-month-old infant with genetically confirmed PWS who underwent bilateral orchidopexy under general anesthesia. The patient’s preoperative evaluation revealed significant hypotonia and a predisposition to respiratory complications. During the procedure, advanced airway management techniques, including the use of C-MAC and high-flow nasal oxygenation (HFNO), were employed to alleviate the risk of difficult airway and respiratory failure. The anesthesia team meticulously monitored the patient's vital signs and thermoregulation throughout the surgery to prevent arrhythmias and other complications associated with PWS.The successful anesthetic management of a child with Prader-Willi syndrome requires a multidisciplinary approach, thorough preoperative planning, meticulous intraoperative monitoring, and vigilant postoperative management to minimize the risk of complications in this vulnerable patient population.
 

Keywords: Pradder- Wili syndrome, Hypotonia, Obstructive sleep apnea, C- MAC, Noninvasive ventilation, Neurodevelopmental disorder, Anesthetic management

How to cite : Singh A, Gaba P, Sharma K, Gupta L, High flow nasal oxygenation and videolaryngoscopy - the two saviours in a case of Prader-Willi syndrome: A case report. Indian J Clin Anaesth 2024;11(4):608-610

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